Osteogenesis imperfecta is a genetic disease caused by defects in the synthesis of type I collagen; clinical characteristics are short stature, blue or gray sclera, skeletal deformities and bone fragility. We analyzed eight cases of osteogenesis imperfecta with deformities and history of many fractures, for that the Sofield and Millar surgery was performed in 23 bones. After a mean follow up period of ten years and two months, 11 bones did not need revision, twelve bones had 21 complication that needed revision, ten by rod migration, six by refracture, three by new deformities and two by nonunion. There were no cases of infection or neurovascular lesion. This surgery was able to correct deformities, make fracture less frequent and prevent new deformities; revisions were necessary three years and two months after the primary surgery. All patients maintained or improved their ability to walk right after surgery; during the follow up, two patients, in which the disease was more severe, had their walking ability decreased and are non ambulatory now.
Osteogenesis imperfecta; gait; osteotomy
